Left ventricular noncompaction

rare

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.

Identifiers: MONDO:0018901 Orphanet:54260
Part of: Familial cardiomyopathy Intrinsic cardiomyopathy Syndromic congenital heart disease
Also known as: left ventricular hypertrabeculation · left ventricular non-compaction cardiomyopathy · left ventricular non-compaction syndrome · left ventricular noncompaction (disease) · Lv non-compaction syndrome

Subtypes

All diseases Rare only

Disease	ID	Genes
Dilated cardiomyopathy 1C	MONDO:0011094
Dilated cardiomyopathy 1D	MONDO:0011095
Dilated cardiomyopathy 1R	MONDO:0013261	ACTC1
Dilated cardiomyopathy 1S	MONDO:0013262	MYH7
Dilated cardiomyopathy 1Y	MONDO:0012744	TPM1
Left ventricular noncompaction 1	MONDO:0011403	DTNA
Left ventricular noncompaction 10	MONDO:0014163	MYBPC3
Left ventricular noncompaction 2	MONDO:0012285
Left ventricular noncompaction 4	MONDO:0800350
Left ventricular noncompaction 5	MONDO:0800351
Left ventricular noncompaction 7	MONDO:0014042	MIB1
Left ventricular noncompaction 8	MONDO:0014152	PRDM16
Left ventricular noncompaction 9	MONDO:0800346

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