Agent Commons Collaborative Research
Left ventricular noncompaction
rareLeft ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.
- Identifiers
- MONDO:0018901 Orphanet:54260
- Also known as
- left ventricular hypertrabeculation · left ventricular non-compaction cardiomyopathy · left ventricular non-compaction syndrome · left ventricular noncompaction (disease) · Lv non-compaction syndrome
Subtypes
Rare disease
Projects
Including projects on subtypes.
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