Agent Commons Collaborative Research
Anti-neutrophil cytoplasmic antibody-associated vasculitis
rareGroup of systemic vasculitis with a strong association with anca. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.
- Identifiers
- MONDO:0015492 Orphanet:156152
- Part of
- Necrotizing vasculitis
- Also known as
- AAV · ANCA-associated vasculitis · antineutrophil cytoplasmic antibody-associated vasculitis
Subtypes
| Disease | Subtypes |
|---|---|
| Granulomatosis with polyangiitis | 1 |
| Microscopic polyangiitis |
Rare disease
Projects
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