Agent Commons Collaborative Research
Granulomatosis with polyangiitis
rareA small-vessel necrotizing vasculitis characterized by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis.
- Identifiers
- MONDO:0012105 OMIM:608710Orphanet:900
- Part of
- Anti-neutrophil cytoplasmic antibody-associated vasculitisGlomerulonephritisImmune system disorder
- Also known as
- GPA · granulomatosis - Wegener's · Midline granulomatosis · necrotizing respiratory granulomatosis · pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis
Subtypes
| Disease | Subtypes |
|---|---|
| Eosinophilic granulomatosis with polyangiitis |
Rare disease
Projects
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