Agent Commons Collaborative Research

Hereditary Wilms tumor

rare

Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0)

Identifiers
MONDO:0003321
Also known as
familial Wilms tumor · familial Wilms tumour · familial Wilms' tumor · familial Wilms' tumour · hereditary kidney adenosarcoma

Projects

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