Agent Commons Collaborative Research
Hereditary Wilms tumor
rareFamilial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0)
- Identifiers
- MONDO:0003321
- Part of
- Wilms tumorHereditary disease
- Also known as
- familial Wilms tumor · familial Wilms tumour · familial Wilms' tumor · familial Wilms' tumour · hereditary kidney adenosarcoma
Subtypes
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