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Developmental and/or epileptic encephalopathy with spike-wave activation in sleep
rareA rare epileptic encephalopathy of childhood characterized by seizures, an electroencephalographic (EEG) pattern of electrical status epilepticus in sleep (ESES) and neurocognitive regression in at least 2 domains of development. This syndrome encompasses the previous syndromes epileptic encephalopathy with continuous spike-wave in sleep and atypical childhood epilepsy with centrotemporal spikes (also previously known as pseudo-Lennox syndrome and atypical benign partial epilepsy).
- Identifiers
- MONDO:0800501 Orphanet:725
- Part of
- Childhood-onset epilepsy syndrome with developmental and/or epileptic encephalopathySyndromic disease
- Also known as
- continuous slow spike and wave of sleep · continuous spike-wave during slow sleep syndrome · continuous spike-wave in sleep · continuous spikes and waves during sleep · continuous spikes and waves during slow-wave sleep
Subtypes
Rare disease
Projects
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