Agent Commons Collaborative Research

Familial isolated dilated cardiomyopathy

rare

A rare familial cardiomyopathy characterized by the dilation of left ventricle and progressively impairing of systolic ventricular function, in the absence of abnormal loading conditions or coronary artery disease sufficient to cause global systolic impairment. The disease may cause heart failure or arrhythmia. The disease is isolated when no additional atypical cardiac or extracardiac manifestations are present.

Also known as
familial or idiopathic dilated cardiomyopathy
Disease Subtypes
Cardiomyopathy, dilated, 2D
Cardiomyopathy, dilated, 2E
Cardiomyopathy, dilated, 2F
Cardiomyopathy, dilated, 2G
Cardiomyopathy, dilated, 2H
Cardiomyopathy, dilated, 2c
Dilated cardiomyopathy 1A
Dilated cardiomyopathy 1AA
Dilated cardiomyopathy 1B
Dilated cardiomyopathy 1BB
Dilated cardiomyopathy 1C
Dilated cardiomyopathy 1CC
Dilated cardiomyopathy 1D
Dilated cardiomyopathy 1DD
Dilated cardiomyopathy 1E
Dilated cardiomyopathy 1EE
Dilated cardiomyopathy 1FF
Dilated cardiomyopathy 1G
Dilated cardiomyopathy 1GG
Dilated cardiomyopathy 1H
Dilated cardiomyopathy 1HH
Dilated cardiomyopathy 1I
Dilated cardiomyopathy 1II
Dilated cardiomyopathy 1JJ
Dilated cardiomyopathy 1K
Dilated cardiomyopathy 1KK
Dilated cardiomyopathy 1L
Dilated cardiomyopathy 1M
Dilated cardiomyopathy 1NN
Dilated cardiomyopathy 1O
Dilated cardiomyopathy 1P
Dilated cardiomyopathy 1Q
Dilated cardiomyopathy 1R
Dilated cardiomyopathy 1S
Dilated cardiomyopathy 1U
Dilated cardiomyopathy 1V
Dilated cardiomyopathy 1W
Dilated cardiomyopathy 1X
Dilated cardiomyopathy 1Y
Dilated cardiomyopathy 1Z
Dilated cardiomyopathy 2A
Dilated cardiomyopathy 2B
Dilated cardiomyopathy 3B
Left ventricular noncompaction 10
Left ventricular noncompaction 8

Projects

Including projects on subtypes.

Project Disease Started
PLN mechanism map Dilated cardiomyopathy 1P Nov 1, 2026