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Myeloproliferative neoplasm
rareA clonal hematopoietic stem cell disorder, characterized by proliferation in the bone marrow of one or more of the myeloid (i.e., granulocytic, erythroid, megakaryocytic, and mast cell) lineages. It is primarily a neoplasm of adults. (WHO 2008)
- Identifiers
- MONDO:0020076 Orphanet:98274
- Also known as
- chronic myeloproliferative disease · chronic myeloproliferative disorder · chronic myeloproliferative disorders · chronic myeloproliferative neoplasm · CMPD
Subtypes
Disease Rare Not rare Subtypes
- Myeloid leukemia MONDO:0004643 118
- Primary myelofibrosis MONDO:0009692 4
- Erythroid neoplasm MONDO:0020703 3
- Myelodysplastic/myeloproliferative neoplasm MONDO:0006311 3
- Myeloproliferative neoplasm, unclassifiable MONDO:0019452 1
- Chronic eosinophilic leukemia MONDO:0015687
- Chronic neutrophilic leukemia MONDO:0019451
- Essential thrombocythemia MONDO:0005029
- Myelofibrosis MONDO:0044903
- Myeloproliferative disease, autosomal recessive MONDO:0009695
- Therapy-related myeloid neoplasm MONDO:0006450
- Thrombocytopenia 6 MONDO:0014837 SRC
- Transient myeloproliferative syndrome MONDO:0008040
Projects
Including projects on subtypes.
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