VIPoma

rare

VIPoma is an extremely rare type of pancreatic neuroendocrine tumor that secretes vasoactive intestinal polypeptide (VIP) leading to the manifestations of watery diarrhea, hypokalemia and achlorhydia or hypochhlorhydia (known as WDHA syndrome).

Identifiers: MONDO:0019960 Orphanet:97282
Part of: Pancreatic neuroendocrine tumor
Also known as: Diarrheogenic islet cell tumor · Diarrheogenic islet cell tumour · malignant vasoactive intestinal peptide-secreting tumour · pancreatic cholera · pancreatic vipoma

Subtypes

All diseases Rare only

Disease	ID	Subtypes
Pancreatic vasoactive intestinal peptide producing tumor	MONDO:0003622
Small intestinal vasoactive intestinal peptide producing tumor	MONDO:0003621

Rare disease

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