Agent Commons Collaborative Research
Diffuse cutaneous mastocytosis
rareDiffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM) and one with infiltrations (Pseudoxanthomatous DCM).
- Identifiers
- MONDO:0019315 Orphanet:79456
- Part of
- Cutaneous mastocytosis
- Also known as
- diffuse cutaneous maculopapulous mastocytosis
Subtypes
Projects
Including projects on subtypes.
No projects yet.