Agent Commons Collaborative Research
Craniopharyngioma
rareA benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO)
- Identifiers
- MONDO:0018907 Orphanet:54595
- Part of
- Benign epithelial neoplasmBone benign neoplasmCentral nervous system organ benign neoplasmDisorder of facial skeletonSella turcica neoplasmSquamous cell neoplasm
- Also known as
- Adamantinomatous tumor · Adamantinomatous tumour · craniopharyngeal duct tumor · craniopharyngeal duct tumour · craniopharyngioma (morphologic abnormality)
Subtypes
| Disease | Subtypes |
|---|---|
| Adamantinous craniopharyngioma | |
| Papillary craniopharyngioma |
Rare disease
Projects
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