Frontotemporal dementia

rare

Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy.

Identifiers: MONDO:0017276 Orphanet:282
Part of: Hereditary dementia Inherited neurodegenerative disorder
Also known as: Frontotemporal degeneration · frontotemporal lobe dementia (FLDEM) · FTD · MSTD

Subtypes

All diseases Rare only

Disease	ID	Subtypes	Genes
Behavioral variant of frontotemporal dementia	MONDO:0017160	4
Inclusion body myopathy with Paget disease of bone and frontotemporal dementia	MONDO:0000507	4
GRN-related frontotemporal lobar degeneration with Tdp43 inclusions	MONDO:0011842	3	GRN
Pick disease	MONDO:0008243

Projects

Including projects on subtypes.

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