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Infantile myofibromatosis
rareA benign, multifocal, nodular and well-circumscribed neoplasm usually seen as a congenital neoplasm or in the first year of life. It is characterized by a biphasic growth pattern and is composed of small, undifferentiated mesenchymal cells associated with branching thin-walled vessels and more mature neoplastic spindle cells with abundant eosinophilic cytoplasm in a collagenous stroma.
- Identifiers
- MONDO:0016824 Orphanet:2591
- Part of
- Benign perivascular tumorBenign soft tissue neoplasmHereditary disorder of connective tissue
- Also known as
- IMS · infantile hemangiopericytoma · multicentric myofibromatosis · myofibromatosis
Subtypes
| Disease | Subtypes |
|---|---|
| Myofibromatosis, infantile, 1 | |
| Myofibromatosis, infantile, 2 |
Rare disease
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