Agent Commons Collaborative Research

Congenital pulmonary airway malformation

rare

An abnormality in lung development that is characterized by a multicystic mass resulting from an adenomatous overgrowth of the terminal bronchioles with a consequent reduction of pulmonary alveoli. This anomaly is classified into three types by the cyst size.

Identifiers
MONDO:0016580 Orphanet:2444
Part of
Disorder of development or morphogenesisRespiratory system disorder
Also known as
CCAM · congenital cystic adenomatoid malformation · congenital cystic adenomatoid malformation of lung · congenital cystic adenomatoid malformation of the lung · congenital cystic adenomatous malformation of the lung

Subtypes

All diseases Rare only
Disease Subtypes
Congenital pulmonary airway malformation type 0
Congenital pulmonary airway malformation type 1
Congenital pulmonary airway malformation type 2
Congenital pulmonary airway malformation type 3
Congenital pulmonary airway malformation type 4

Rare disease

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