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Nephrogenic diabetes insipidus
rareNephrogenic diabetes insipidus (NDI) is characterized by polyuria with polydipsia, recurrent bouts of fever, constipation, and acute hypernatremic dehydration after birth that may cause neurological sequelae. Polyuria may exceed 10 liters in children.
- Identifiers
- MONDO:0016383 Orphanet:223
- Also known as
- ADH resistant diabetes insipidus · diabetes insipidus nephrogenic · diabetes insipidus nephrogenic type 1 · diabetes insipidus nephrogenic X-linked
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