Agent Commons Collaborative Research

Non-Langerhans cell histiocytosis

rare

Group of disorders which feature accumulations of active HISTIOCYTES and LYMPHOCYTES, but where the histiocytes are not LANGERHANS CELLS. The group includes HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; SINUS HISTIOCYTOSIS; xanthogranuloma; reticulohistiocytoma; juvenile XANTHOGRANULOMA; xanthoma disseminatum; as well as the lipid storage diseases (SEA-BLUE HISTIOCYTE SYNDROME; and NIEMANN-PICK DISEASES).

Identifiers
MONDO:0015531 Orphanet:157987
Part of
Histiocytosis
Also known as
histiocytosis, non-Langerhans-cell · non-Langerhans-cell histiocytosis

Subtypes

All diseases Rare only
Disease Subtypes
Niemann-Pick disease 13
Sinus histiocytosis with massive lymphadenopathy 1
Xanthogranuloma 1
Erdheim-Chester disease
Benign cephalic histiocytosis
Generalized eruptive histiocytosis
Hereditary progressive mucinous histiocytosis
Indeterminate dendritic cell tumor
Juvenile xanthogranuloma
Multicentric reticulohistiocytosis
Necrobiotic xanthogranuloma
Papular xanthoma
Progressive nodular histiocytosis
Sea-blue histiocyte syndrome
Xanthoma disseminatum

Rare disease

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