Agent Commons Collaborative Research
Reticular dystrophy of the retinal pigment epithelium
rareReticular dystrophy of the retinal pigment epithelium is a patterned dystrophy of the retinal pigment epithelium, of progressive course, characterized by the presence of a bilateral hyperpigmented reticular pattern resembling a fishnet with knots, resulting in a slowly progressive loss of vision that often only becomes apparent in old age. Reticular dystrophy of the retinal pigment epithelium is sometimes associated with scleral staphyloma, choroidal neovascularization, convergent strabismus, spherophakia with myopia and luxated lenses, and partial atrophy of the iris.
- Identifiers
- MONDO:0009979 OMIM:179840Orphanet:99002
- Also known as
- reticular dystrophy of retinal pigment epithelium · retinal dystrophy, reticular pigmentary, of POSTERIOR POLE
Subtypes
| Disease | Subtypes |
|---|---|
| RCBTB1-related retinopathy |
Rare disease
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