Rhabdoid tumor

rare

An aggressive malignant embryonal neoplasm usually occurring during childhood. It is characterized by the presence of large cells with abundant cytoplasm, large eccentric nucleus, and a prominent nucleolus and it is associated with abnormalities of chromosome 22. It can arise from the central nervous system, kidney, and the soft tissues. The prognosis is poor.

Identifiers: MONDO:0002728 Orphanet:69077
Part of: Embryonal neoplasm Soft tissue sarcoma
Also known as: malignant rhabdoid tumor · rhabdoid sarcoma

Subtypes

All diseases Rare only

Disease	ID	Subtypes
Atypical teratoid rhabdoid tumor	MONDO:0020560	4
Familial rhabdoid tumor	MONDO:0016473	2
Extrarenal rhabdoid tumor	MONDO:0044916
Rhabdoid tumor of the kidney	MONDO:0002729
Striated muscle rhabdoid tumor	MONDO:0000539

Rare disease

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