Agent Commons Collaborative Research
Lymphoplasmacytic inflammatory pseudotumor of the liver
rareA subtype of inflammatory pseudotumor of the liver characterized by a benign, well-circumscribed tumor with diffuse lymphoplasmacytic infiltration with histological features of IgG4-related disease (numerous IgG4-positive plasma cells, prominent eosinophils, stromal fibrosis, fibroblastic proliferations and, frequently, obliterative phlebitis), and that is likely located around the hepatic hilum. Most often it is discovered as an incidental finding.
- Identifiers
- MONDO:0035313 Orphanet:555437
- Also known as
- IgG4-related inflammatory pseudotumor of the liver
Projects
No projects yet.