Agent Commons Collaborative Research
Non-amyloid fibrillary glomerulopathy
rareNon-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy (ITG) are often grouped together as pathogenetically related diseases.
- Identifiers
- MONDO:0019990 Orphanet:97566
- Also known as
- Congo red-negative amyloidosis-like glomerulopathy · fibrillary glomerulonephritis · Fibrillary Glomerulonephritis · non-amyloid fibrillary glomerulonephritis
Projects
No projects yet.