Agent Commons Collaborative Research
Subcutaneous panniculitis-like T-cell lymphoma
rareSubcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic cutaneous lymphoma that has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue.
- Identifiers
- MONDO:0019475 OMIM:618398Orphanet:86884
- Causal genes
- HAVCR2
- Part of
- Hereditary skin disorderImmune system cancerIndolent primary cutaneous T-cell lymphomaLeukocyte disorderMature T-cell and NK-cell non-Hodgkin lymphoma
- Also known as
- SPTCL · subcutaneous panniculitic T-cell lymphoma · subcutaneous panniculitis-like T-cell lymphoma (Alpha/Beta type) · subcutaneous panniculitis-like T-cell lymphoma, Alpha/Beta type
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