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CD4+/CD56+ hematodermic neoplasm
rareAn aggressive immature hematologic neoplasm formerly known as blastic NK cell lymphoma, composed of cells with a lymphoblast-like morphology. Recent evidence suggests derivation from a plasmacytoid monocyte. Patients present with cutaneous tumors and bone marrow involvement.
- Identifiers
- MONDO:0019467 Orphanet:86870
- Also known as
- agranular CD4+ CD56+ hematodermic neoplasm/tumor · agranular CD4+ natural Killer cell leukaemia · agranular CD4+ natural Killer cell leukemia · blastic natural Killer leukemia/lymphoma · blastic NK-cell lymphoma
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