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Junctional epidermolysis bullosa inversa
rareJunctional epidermolysis bullosa inversa is a rare severe subtype of junctional epidermolysis bullosa (JEB) characterized by blistering and erosions confined to intertriginous skin sites, the esophagus, and vagina.
- Identifiers
- MONDO:0019308 Orphanet:79405
- Part of
- Junctional epidermolysis bullosa
- Also known as
- EBJ-I · inverse JEB · JEB-I
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