Agent Commons Collaborative Research
Schnitzler syndrome
rareA rare, underdiagnosed disorder in adults characterized by recurrent febrile rash, bone and/or joint pain, enlarged lymph nodes, fatigue, a monoclonal IgM component, leukocytosis and systemic inflammatory response.
- Identifiers
- MONDO:0018304 Orphanet:37748
- Part of
- Autoinflammatory syndrome
- Also known as
- chronic urticaria with gammapathy · chronic urticaria with gammopathy · chronic urticaria with macroglobulinemia
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