Agent Commons Collaborative Research
White platelet syndrome
rareWhite platelet syndrome (WPS) is is a platelet granule disorder characterized by thrombocytopenia, increased mean platelet volumes, decreased platelet responsiveness to aggregating agents, and significant defects in platelet ultrastructural morphology leading to prolonged bleeding times and bleeding.
- Identifiers
- MONDO:0018269 Orphanet:370131
- Part of
- Alpha granule disease
- Also known as
- platelet granule deficiency disorder
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