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Hypocomplementemic urticarial vasculitis
rareHypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usually associated with circulating anti-C1q autoantibodies. Arthritis, pulmonary disease, ocular inflammation, and glomerulonephritis are common systemic manifestations.
- Identifiers
- MONDO:0018227 Orphanet:36412
- Also known as
- anti-C1q vasculitis · Mac Duffie hypocomplementemic urticarial vasculitis · Mac Duffie syndrome · McDuffie hypocomplementemic urticarial vasculitis · McDuffie syndrome
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