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POEMS syndrome
rarePOEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.
- Identifiers
- MONDO:0017364 Orphanet:2905
- Part of
- Acquired peripheral neuropathyLeukocyte disorderParaneoplastic hematological syndromeParaneoplastic neurologic syndromeParneoplastic endocrine syndrome
- Also known as
- Crow-Fukase syndrome · osteosclerotic myeloma · PEP syndrome · polyneuropathy organomegaly · polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes syndrome
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