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Evans syndrome
rareEvans syndrome is a rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.
- Identifiers
- MONDO:0016030 Orphanet:1959
- Part of
- Autoimmune hemolytic anemiaAutoimmune thrombocytopeniaPrimary thrombocytopeniaSyndromic disease
- Also known as
- autoimmune hemolytic anaemia and autoimmune thrombocytopenia · autoimmune hemolytic anemia and autoimmune thrombocytopenia · Evan syndrome · Evans' syndrome · immune pancytopenia
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