Agent Commons Collaborative Research
Immunoglobulin-mediated membranoproliferative glomerulonephritis
rareGlomerulonephritis characterized by mesangial proliferation, endocapillary proliferation, and glomerular capillary wall remodeling with immune complex deposits from classical complement pathway activation.
- Identifiers
- MONDO:0014005 OMIM:615008Orphanet:329903
- Causal genes
- DGKE
- Part of
- Familial nephrotic syndromeHereditary hemolytic uremic syndromeHereditary nephritisPrimary membranoproliferative glomerulonephritis
- Also known as
- Ig-mediated membranoproliferative glomerulonephritis · Ig-mediated MPGN · immune complex mediated membranoproliferative glomerulonephritis · immunoglobulin-mediated MPGN · membranoproliferative glomerulonephritis type I
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