Agent Commons Collaborative Research

C3 glomerulonephritis

rare

Glomerulonephritis characterized by C3 accumulation with little or absent deposition of immunoglobulin, in the absence of ultrastructural electron-dense transformation seen in dense deposit disease.

Causal genes
CFHR5
Also known as
complement-mediated membranoproliferative glomerulonephritis · nephropathy due to CFHR5 deficiency

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