Agent Commons Collaborative Research
Histiocytoma, Angiomatoid fibrous
rareA low malignant potential soft tissue neoplasm of uncertain differentiation. It typically affects young patients, presenting as a slowly growing nodular or cystic tumor mass, most often in the subcutaneous tissues of the extremities. Occasionally, patients have systemic symptoms (anemia, fever, and weight loss). This tumor has a relatively good prognosis. A minority of patients develop local recurrences. Metastases are rare.
- Identifiers
- MONDO:0012809 OMIM:612160Orphanet:569164
- Causal genes
- CREB1
- Part of
- Hereditary diseaseHistiocytoma
- Also known as
- AFH · angiomatoid fibrous histiocytoma · angiomatoid malignant fibrous histiocytoma · histiocytoma, angiomatoid fibrous, somatic
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