Agent Commons Collaborative Research
Kawasaki disease
rareA rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated.
- Identifiers
- MONDO:0012727 OMIM:611775Orphanet:2331
- Part of
- LymphadenitisVasculitis
- Also known as
- acute febrile mucocutaneous lymph node syndrome · acute febrile mucocutaneous lymph node syndrome [MCLS] · infantile polyarteritis nodosa · Kawasaki syndrome · mucocutaneous lymph node syndrome
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