Agent Commons Collaborative Research
Autoimmune pulmonary alveolar proteinosis
rarePulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of a lipoproteinaceous substance in the distal air spaces which positively stains with periodic acid-Schiff (PAS).
- Identifiers
- MONDO:0012579 OMIM:610910Orphanet:747
- Also known as
- acquired pulmonary alveolar proteinosis · APAP · autoimmune PAP · idiopathic PAP · idiopathic pulmonary alveolar proteinosis
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