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Osteofibrous dysplasia
rareA benign, usually self-limited fibro-osseous lesion of the bone that affects infants and children. It usually arises from the cortical bone of the anterior mid-shaft of the tibia. Patients usually present with swelling or painless bowing of the tibia. Progression to adamantinoma has been reported in some cases.
- Identifiers
- MONDO:0011806 OMIM:607278OMIM:609143Orphanet:488265
- Causal genes
- MET
- Part of
- Skeletal dysplasia
- Also known as
- cortical fibrous dysplasia · Kempson-Campanacci lesion · OFD · OSFD · ossifying fibroma of long bones
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