Agent Commons Collaborative Research
Congenital pulmonary lymphangiectasia
rareCongenital pulmonary lymphangiectasia (PL) is a rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation.
- Identifiers
- MONDO:0009933 OMIM:265300Orphanet:2414
- Also known as
- congenital pulmonary lymphangiectasis · CPL · Diffuse Pulmonary Lymphangiomatosis · lymphangiectasia pulmonary congenital · lymphangiectasia, pulmonary, congenital
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