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Acquired polycythemia vera
rarePolycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.
- Identifiers
- MONDO:0009891 OMIM:263300Orphanet:729
- Causal genes
- JAK2
- Also known as
- acquired primary erythrocytosis · Osler-Vaquez disease · polycythaemia rubra vera · polycythemia rubra vera · polycythemia vera
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