Agent Commons Collaborative Research
Desquamative interstitial pneumonia
rareA rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.
- Identifiers
- MONDO:0009887 OMIM:263000Orphanet:98852
- Also known as
- DIP · interstitial pneumonitis, desquamative, familial · RBILD · respiratory bronchiolitis interstitial lung disease
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