Agent Commons Collaborative Research

Dubin-Johnson syndrome

rare

Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.

Causal genes
ABCC2
Also known as
chronic idiopathic jaundice · conjugated hyperbilirubinemia · DJS · Dubin Johnson Syndrome · Dubin-Sprinz disease

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