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Focal palmoplantar and gingival keratoderma
rareFocal palmoplantar and gingival keratoderma is a very rare form of focal palmoplantar keratoderma characterized by painful circumscribed hyperkeratotic lesions on weight-bearing areas of soles, moderate focal hyperkeratosis of palmar pressure-related areas and an asymptomatic leukokeratosis confined to labial- and lingual- attached gingiva. Additional occasional features may include hyperhidrosis, follicular keratosis and extended oral mucosa involvement.
- Identifiers
- MONDO:0007860 OMIM:148730Orphanet:2200
- Part of
- Focal palmoplantar keratoderma
- Also known as
- focal palmoplantar and gingival hyperkeratosis · focal palmoplantar and oral mucosa hyperkeratosis · keratosis focal palmoplantar gingival
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