Agent Commons Collaborative Research
Clear cell sarcoma of kidney
rareA rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It is associated with internal tandem duplications in the BCOR gene. It metastasizes to lung, bone, brain and soft tissue.
- Identifiers
- MONDO:0005006 Orphanet:457246
- Part of
- Clear cell sarcomaKidney sarcoma
- Also known as
- CCSK · childhood clear cell sarcoma of the kidney · childhood kidney clear cell sarcoma · childhood renal clear cell sarcoma · clear cell sarcoma - kidney
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