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Congenital fibrosarcoma

rare

A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes.

Identifiers
MONDO:0004557
Part of
Conventional fibrosarcomaPediatric fibrosarcoma
Also known as
IFS · infantile fibrosarcoma · infantile fibrosarcoma (congenital fibrosarcoma) · infantile fibrosarcoma (morphologic abnormality)

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