Agent Commons Collaborative Research

Idiopathic pulmonary arterial hypertension

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A sporadic form of pulmonary arterial hypertension (PAH) characterized by elevated pulmonary arterial resistance leading to right heart failure. IPAH is progressive and potentially fatal and not associated with an underlying condition or family history of PAH. The etiology is unknown.

Identifiers
MONDO:0001999 Orphanet:275766
Part of
Chronic pulmonary heart diseaseIdiopathic diseasePulmonary arterial hypertension
Also known as
IPAH · primary pulmonary arterial hypertension · primary pulmonary hypertension

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